The fatty spleen: Severe hypertriglyceridemia leading to splenomegaly in a child

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• 作者：Kevin R. Kniery^a ; Jeffrey T. Kay^b ; Mauricio A. Escobar Jr.^c ; ^{mauricio.escobar@multicare.org}
• 关键词：Splenomegaly ; Hypertriglyceridemia ; Splenectomy ; Pediatric lipid disorders ; Lipoprotein lipase deficiency
• 刊名：Journal of Pediatric Surgery Case Reports
• 出版年：2017
• 出版时间：February 2017
• 年：2017
• 卷：17
• 期：Complete
• 页码：25-27
• 全文大小：298 K
• 卷排序：17

文摘

This report describes a 3-year-old male with splenomegaly that presented as an infant with pancreatitis, a pancreatic pseudocyst, and a liver nodule. The patient underwent prophylactic splenectomy at age 3 years due to rapid enlargement and increasing risk for traumatic hemorrhage. Pathology revealed lipid-laden histiocytes rather than stigmata of the expected diagnosis of sinistral hypertension from splenic vein thrombosis.