Proboscis lateralis with ipsilateral sinonasal and olfactory pathway aplasia

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• 作者：Sanjay Vaid ; Darshan Shah ; Sudarshan Rawat ; Rahul Shukla
• 关键词：Imaging ; Proboscis lateralis ; Hemisinonasal aplasia ; Olfactory pathway ; HRCT ; MRI
• 刊名：Journal of Pediatric Surgery
• 出版年：2010
• 出版时间：February 2010
• 年：2010
• 卷：45
• 期：2
• 页码：453-456
• 全文大小：438 K

文摘

Proboscis lateralis is a rare craniofacial malformation characterized by absence of nasal cavity on one side with a trunk-like nasal appendage protruding from superomedial portion of the ipsilateral orbit. High-resolution computed tomography and magnetic resonance imaging are extremely useful in evaluating this congenital condition and the wide spectrum of associated anomalies occurring in the surrounding anatomical regions and brain. We present a case of proboscis lateralis in a 2-year-old girl with associated ipsilateral sinonasal aplasia, orbital cyst, absent olfactory bulb and olfactory tract. Absence of ipsilateral olfactory pathway in this rare disorder has been documented on high-resolution computed tomography and magnetic resonance imaging by us for the first time in English medical literature.