Meconium thorax: A case of bochdalek hernia and cecal perforation in a neonate with Job's syndrome

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• 作者：Sonia A. Butterworth ; Eric M. Webber
• 关键词：Tissue engineering ; mesenchymal stem cells ; bone marrow-derived stromal cells ; cartilage ; tracheal malformations ; fetal surgery ; congenital anomalies ; transplantation
• 刊名：Journal of Pediatric Surgery
• 出版年：2002
• 出版时间：April 2002
• 年：2002
• 卷：37
• 期：4
• 页码：673-674
• 全文大小：68 K

文摘

Meconium peritonitis most often is associated with congenital intestinal obstruction and meconium ileus. Uncommonly, other etiologies are identified. Hyperimmunoglobulin E syndrome (Job's syndrome) is a rare genetic disorder that is characterized by recurrent staphylococcal respiratory and skin infections in addition to elevated serum IgE levels. There have been 2 previously reported cases of intestinal complications associated with Job's syndrome. The current case is the third such case and is the first report of meconium peritonitis in a patient with hyperimmunoglobulin E syndrome. The patient presented with a meconium thorax as a result of a concurrent congenital diaphragmatic hernia.