We report a 3-month-old female infant with giant immature teratoma derived from the hepatoduodenal ligament. The tumor was very large and the serum alpha-fetoprotein level was high, and it was initially misdiagnosed as hepatoblastoma at another hospital. However, it was confirmed to be an extrahepatic tumor by abdominal CT and ultrasonography at our institute.
We performed laparotomy and the frozen section of biopsied specimen revealed the tumor to be a teratoma. The tumor originated from the hepatoduodenal ligament and was excised. The final pathological diagnosis was immature teratoma with focal embryoid components.