Cardiovascular magnetic resonance demonstration of the spectrum of morphological phenotypes and patterns of myocardial scarring in Anderson-Fabry disease

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• 作者：Djeven Parameshvara Deva ; Kate Hanneman…
• 关键词：Cardiomyopathy ; Hypertrophy ; Cardiovascular magnetic resonance ; Anderson ; Fabry disease ; Left ventricular morphology ; Myocardial scar ; Late gadolinium enhancement
• 刊名：Journal of Cardiovascular Magnetic Resonance
• 出版年：2017
• 出版时间：January 2017
• 年：2017
• 卷：18
• 期：1
• 全文大小：3,425 KB
• 刊物主题：Imaging / Radiology; Angiology; Cardiology;
• 出版者：BioMed Central
• ISSN：1532-429X
• 卷排序：18

文摘

BackgroundAlthough it is known that Anderson-Fabry Disease (AFD) can mimic the morphologic manifestations of hypertrophic cardiomyopathy (HCM) on echocardiography, there is a lack of cardiovascular magnetic resonance (CMR) literature on this. There is limited information in the published literature on the distribution of myocardial fibrosis in patients with AFD, with scar reported principally in the basal inferolateral midwall.