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Wiley电子期刊(4)	SpringerLink电子期刊(211)	ACS电子期刊(4)
Springer电子图书(11)	Elsevier电子期刊(385)

在“Elsevier电子期刊”中，命中：385条，耗时：小于0.01 秒

在所有数据库中总计命中：615条

1.Deficiency of glycerol-3-phosphate acyltransferase 1 decreases triacylglycerol storage and induces fatty acid oxidation in insect fat body

作者：Michele Alves-Bezerra^a ; ^b ; Isabela B. Ramos^a ; Iron F. De Paula^a ; Clarissa M. Maya-Monteiro^c ; Eric L. Klett^b ; ^d ; Rosalind A. Coleman^b ; Katia C. Gondim^a ; ^{katia@bioqmed.ufrj.br}

关键词：ACBP1 ; acyl-CoA-binding protein 1 ; ACSL1 ; acyl-CoA synthetase 1 ; BAT ; brown adipose tissue ; CPT1 ; carnitine palmitoyltransferase 1 ; DAG ; diacylglycerol ; ER ; endoplasmic reticulum ; G3P ; glycerol-3-phosphate ; GPAT ; glycerol-3-phosphate acyltransferase ; LD ; lipid droplet ; LPA ; lysophosphatidic acid ; NEM ; N-ethylmaleimide ; PA ; phosphatidic acid ; PL ; phospholipid ; TAG ; triacylglycerol

刊名：Biochimica et Biophysica Acta (BBA) - Molecular and Cell Biology of Lipids

出版年：2017

2.Clinical Features of Carnitine Deficiency Secondary to Pivalate-Conjugated Antibiotic Therapy

作者：Hironori Kobayashi ; MD ; PhD ; ^{bakki@med.shimane-u.ac.jp" class="auth_mail" title="E-mail the corresponding author} ; Seiji Fukuda ; MD ; PhD ; Kenji Yamada ; MD ; Yuki Hasegawa ; MD ; PhD ; Tomoo Takahashi ; MD ; Jamiyan Purevsuren ; MD ; PhD ; Seiji Yamaguchi ; MD ; PhD

关键词：carnitine deficiency ; pivalate ; pivoxil group ; pivalate-conjugated antibiotics ; acute encephalopathy ; hypoglycemia ; fatty acid oxidation

刊名：The Journal of Pediatrics

出版年：2016

3.Five novel SUCLG1 mutations in three Chinese patients with succinate-CoA ligase deficiency noticed by mild methylmalonic aciduria

作者：Yupeng Liu ; Xiyuan Li ; Qiao Wang ; Yuan Ding ; Jinqing Song ; Yanling Yang ; ^{organic.acid@126.com" class="auth_mail" title="E-mail the corresponding author} ; ^{yanlingy@vip.sina.com" class="auth_mail" title="E-mail the corresponding author}

关键词：Methylmalonic aciduria ; Succinate-CoA ligase deficiency ; Encephalomyopathy ; Mitochondrial DNA depletion ; SUCLG1

刊名：Brain and Development

出版年：2016

4.iPLA2β deficiency attenuates obesity and hepatic steatosis in ob/ob mice through hepatic fatty-acyl phospholipid remodeling

作者：Xiuling Deng^a ; ^b ; Jiliang Wang^a ; Li Jiao^a ; Tanyarath Utaipan^a ; Sabine Tuma-Kellner^a ; Gerd Schmitz^c ; Gerhard Liebisch^c ; Wolfgang Stremmel^a ; Walee Chamulitrat^a ; ^{Walee.Chamulitrat@med.uni-heidelberg.de" class="auth_mail" title="E-mail the corresponding author}

关键词：AA ; arachidonic acid ; Acox1 ; acyl-CoA oxidase ; ATGL ; adipocyte triglyceride lipase ; CCTα ; phosphate cytidylyltransferase 1 ; choline α ; CEPT ; choline/ethanolaminephosphotransferase 1 ; CE ; cholesterol esters ; CHOL ; cholesterol ; CM ; chylomicrons ; CPT1 ; carnitine palmitoyltransferase ; Crot ; carnitine octanoyltransferase ; CK ; choline kinase ; DGAT ; diacylglycerol acyltransferase ; DHA ; docosahexaenoic acid ; EPA ; eicosapentaenoic acid ; EK ; ethanolamine kinase ; HOMA-IR ; homeostasis model assessment-insul

刊名：Biochimica et Biophysica Acta (BBA)-Molecular and Cell Biology of Lipids

出版年：2016

5.Levocarnitine Improves Cardiac Function in Hemodialysis Patients With Left Ventricular Hypertrophy: A Randomized Controlled Trial

作者：Terumi Higuchi ; MD ; PhD¹ ; Masanori Abe ; MD ; PhD² ; ^{abe.masanori@nihon-u.ac.jp" class="auth_mail" title="E-mail the corresponding author} ; Toshio Yamazaki ; MD¹ ; Erina Okawa ; MD¹ ; Hideyuki Ando ; MD³ ; Sunao Hotta ; PhD⁴ ; Osamu Oikawa ; MD ; PhD² ; Fumito Kikuchi ; MD ; PhD⁵ ; Kazuyoshi Okada ; MD ; PhD² ; Masayoshi Soma ; MD ; PhD⁶

关键词：Carnitine ; cardiac function ; cardiac morphology ; ejection fraction (EF) ; levocarnitine ; hemodialysis (HD) ; left ventricular hypertrophy (LVH) ; left ventricular mass index (LVMI) ; N-terminal pro&ndash ; brain natriuretic peptide (NT-proBNP) ; end-stage renal disease (ESRD) ; randomized controlled trial (RCT)

刊名：American Journal of Kidney Diseases

出版年：2016

6.Disorders of carnitine biosynthesis and transport

作者：Ayman W. El-Hattab^a ; Fernando Scaglia^b ; ^{fscaglia@bcm.edu" class="auth_mail" title="E-mail the corresponding author}

关键词：Systemic carnitine deficiency ; Carnitine transport defect ; Autism spectrum disorders ; Cardiomyopathy ; Fatty acid oxidation

刊名：Molecular Genetics and Metabolism

出版年：2015

7.Vitamin D deficiency impairs glucose-stimulated insulin secretion and increases insulin resistance by reducing PPAR-γ expression in nonobese Type 2 diabetic rats

作者：Sunmin Park ; ^{smpark@hoseo.edu" class="auth_mail" title="E-mail the corresponding author} ; Da Sol Kim ; Suna Kang

关键词：Vitamin D ; Insulin resistance ; Insulin secretion ; Energy expenditure ; Lean body mass ; PPAR-γ

刊名：Journal of Nutritional Biochemistry

出版年：2016

8.Quantification of hypoglycin A as butyl ester

作者：Johannes Sander^a ; ^{j.sander@metabscreen.de" class="auth_mail" title="E-mail the corresponding author} ; Michael Terhardt^a ; Stefanie Sander^a ; Nils Janzen^a ; ^b

关键词：AM ; atypical myopathy in horses ; HGA ; hypoglycin A (l-α-amino-methylenecyclopropyl propionic acid) ; MADD ; multiple acyl carnitine dehydrogenase deficiency ; MCPA ; methylenecyclopropylacetic acid

刊名：Journal of Chromatography B, Analytical Technologies in the Biomedical and Life Sciences

出版年：2016

9.cis-4-Decenoic and decanoic acids impair mitochondrial energy, redox and Ca^{2 +} homeostasis and induce mitochondrial permeability transition pore opening in rat brain and liver: Possible implications for the pathogenesis of MCAD deficiency

作者：Alexandre Umpierrez Amaral^a ; Cristiane Cecatto^a ; Janaí ; na Camacho da Silva^a ; Alessandro Wajner^a ; Ká ; lita dos Santos Godoy^a ; Rafael Teixeira Ribeiro^a ; Moacir Wajner^a ; ^b ; ^{mwajner@ufrgs.br" class="auth_mail" title="E-mail the corresponding author}

关键词：AA ; antimycin A ; ANT ; adenine nucleotide translocator ; ATC ; atractyloside ; BSA ; bovine serum albumin ; CCCP ; carbonyl cyanide 3-chlorophenyl hydrazine ; cDA ; cis-4-decenoic acid ; CsA ; cyclosporin A ; DA ; decanoic acid ; DC ; decanoylcarnitine ; EGTA ; ethylene glycol-bis (2-aminoethylether)-NN ; N&prime ; N&prime ; -tetraacetic acid ; EtOH ; ethanol ; FAU ; fluorescence arbitrary units ; GP ; generalized polarization ; HEPES ; N-[2-hydroxyethyl]piperazine-N&prime ; -[2-ethane-sulfonic acid] ; MDA ; malondialdehyde ; MC

刊名：Biochimica et Biophysica Acta (BBA) - Bioenergetics

出版年：2016

10.Lipolysis and lipophagy in lipid storage myopathies

作者：Corrado Angelini^a ; ^{corrado.angelini@unipd.it" class="auth_mail" title="E-mail the corresponding author} ; Anna Chiara Nascimbeni^b ; Giovanna Cenacchi^c ; Elisabetta Tasca^a

关键词：ATGL ; adipose triglyceride lipase ; ATP-ase ; adenosine tri-phosphatase ; CD ; carnitine deficiency ; CK ; creatine kinase ; COX ; cytochrome oxidase ; CPT ; carnitine-palmitoyl-transferase ; DAPI ; 4&prime ; 6-diamidin-2-phenylindole ; EMG ; electromyography ; ETF ; electron transfer flavoprotein ; FOXO ; fork head box protein ; GAPDH ; glyceraldehyde 3-phosphate dehydrogenase ; HSL ; hormone-sensitive lipase ; LC3 ; microtubule-associated proteins light chain-3 ; LSM ; lipid storage myopathy ; MADD ; multiple acyl-CoA deh

刊名：Biochimica et Biophysica Acta (BBA) - Molecular Basis of Disease

出版年：2016

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