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Elsevier电子期刊(156)

在“Elsevier电子期刊”中，命中：156条，耗时：小于0.01 秒

在所有数据库中总计命中：156条

1.Structure, biosynthesis and function of unusual lipids A from nodule-inducing and N₂-fixing bacteria

作者：Adam Choma ; ^{adam.choma@poczta.umcs.lublin.pl} ; Iwona Komaniecka ; Kamil Zebracki

关键词：Lipid A ; Nodule-forming bacteria ; Rhizobium ; Very long chain fatty acids (VLCFA)

刊名：Biochimica et Biophysica Acta (BBA) - Molecular and Cell Biology of Lipids

出版年：2017

2.Step changes in leaf oil accumulation via iterative metabolic engineering

作者：Thomas Vanhercke^a ; ¹ ; ^{Thomas.Vanhercke@csiro.au} ; Uday K. Divi^a ; ¹ ; Anna El Tahchy^a ; Qing Liu^a ; Madeline Mitchell^a ; Matthew C. Taylor^b ; Peter J. Eastmond^c ; Fiona Bryant^c ; Anna Mechanicos^a ; Cheryl Blundell^a ; Yao Zhi^a ; ^d ; Srinivas Belide^a ; Pushkar Shrestha^a ; Xue-Rong Zhou^a ; Jean-Philippe Ral^a ; Rosemary G. White^a ; Allan Green^a ; Surinder P. Singh^a ; James R. Petrie^a

关键词：DAG ; diacylglycerol ; DAS ; days after sowing ; DGDG ; digalactosyldiacylglycerol ; DW ; dry weight ; MGDG ; monogalactosyldiacylglycerol ; PC ; phosphatidylcholine ; SDP1 ; Sugar-dependent lipase1 ; TAG ; triacylglycerol ; VLCFA ; very long chain fatty acids

刊名：Metabolic Engineering

出版年：2017

3.Absence of biochemical evidence at an early age delays diagnosis in a patient with a clinically severe peroxisomal biogenesis disorder

作者：Natalia Lü ; sebrink^a ; ^{Natalia.Luesebrink@kgu.de" class="auth_mail" title="E-mail the corresponding author} ; Luciana Porto^b ; Hans R. Waterham^c ; Sacha Ferdinandusse^c ; Hendrik Rosewich^d ; Gerd Kurlemann^e ; Matthias Kieslich^a

关键词：Peroxisomal biogenesis disorder ; Zellweger spectrum disorder ; PEX6 ; Polimicrogyria ; VLCFA

刊名：European Journal of Paediatric Neurology

出版年：2016

4.A new multiplex method for the diagnosis of peroxisomal disorders allowing simultaneous determination of plasma very-long-chain fatty acids, phytanic, pristanic, docosahexaenoic and bile acids by high-performance liquid chromatography-atmospheric pressure chemical ionization-tandem mass spectrometry

作者：Michela Semeraro^a ; ¹ ; ^{michela.semeraro@opbg.net" class="auth_mail" title="E-mail the corresponding author} ; Cristiano Rizzo^a ; ¹ ; Sara Boenzi^a ; Marco Cappa^b ; Enrico Bertini^c ; Giacomo Antonetti^a ; Carlo Dionisi-Vici^a

关键词：PDs ; peroxisomal disorders ; LC-MS/MS ; liquid chromatography-tandem mass spectrometry ; CV ; coefficient of variation ; VLCFAs ; very-long-chain fatty acids ; Pri ; pristanic acid ; PUFAs ; polyunsaturated fatty acids ; DHA ; docosahexaenoic acid ; Phy ; phytanic acid ; PBDs ; peroxisomal biogenesis disorders ; GC&ndash ; MS ; gas chromatography&ndash ; mass spectrometry ; ESI-MS/MS ; electrospray ionization tandem mass spectrometry ; UPLC ; ultra-performance liquid chromatography ; DAABD-AE ; 4-[2-(N ; N-dimethylamino) eth

刊名：Clinica Chimica Acta

出版年：2016

5.Characterization of the role of sphingomyelin synthase 2 in glucose metabolism in whole-body and peripheral tissues in mice

作者：Masayuki Sugimoto^a ; ^b ; Yoichi Shimizu^c ; ^d ; Songji Zhao^e ; Naoyuki Ukon^e ; Ken-ichi Nishijima^a ; ^c ; Masato Wakabayashi^b ; Takeshi Yoshioka^b ; Kenichi Higashino^b ; Yoshito Numata^b ; Tomohiko Okuda^f ; Nagara Tamaki^g ; Hisatoshi Hanamatsu^h ; Yasuyuki Igarashi^h ; Yuji Kuge^a ; ^c ; ^{kuge@ric.hokudai.ac.jp" class="auth_mail" title="E-mail the corresponding author}

关键词：SM ; sphingomyelin ; SMS ; sphingomyelin synthase ; Cer ; ceramide ; CerS ; ceramide synthase ; S1P ; sphingosine 1 phosphate ; LC/ESI-MS/MS ; liquid chromatography/electrospray ionization-tandem mass spectrometry ; VLCFA ; very long-chain fatty acid ; HexCer ; hexosylceramide ; DhCer ; dihydroceramide ; 18F-FDG ; 18F-2-fluoro-2-deoxy-d-glucose ; OGTT ; oral glucose tolerance test ; ITT ; insulin tolerance test ; GSIS ; glucose stimulated-insulin secretion ; HOMA-R ; homeostasis model assessment-insulin resistance ; T2DM

刊名：Biochimica et Biophysica Acta (BBA)-Molecular and Cell Biology of Lipids

出版年：2016

6.Phenotypic variability in a Tunisian family with X-linked adrenoleukodystrophy caused by the p.Gln316Pro novel mutation

作者：Fakhri Kallabi^a ; ^{fakhrikallabi@yahoo.fr" class="auth_mail" title="E-mail the corresponding author} ; Emna Ellouz^b ; Mouna Tabebi^a ; Ghada Ben Salah^c ; Naziha Kaabechi^d ; Leila Keskes^a ; Chahnez Triki^b ; Hassen Kamoun^a ; ^e ; ^{hassen.kamoun@yahoo.fr" class="auth_mail" title="E-mail the corresponding author}

关键词：ABCD1 gene ; Addison disease ; Childhood cerebral ALD ; Novel mutation ; Phenotypic variability ; VLCFA ; X-linked adrenoleukodystrophy

刊名：Clinica Chimica Acta

出版年：2016

7.Peroxisome biogenesis disorders in the Zellweger spectrum: An overview of current diagnosis, clinical manifestations, and treatment guidelines

关键词：AAV ; adeno-associated virus ; AED ; anti-epileptic drug(s) ; DHA ; docosahexaenoic acid ; DHCA ; dihydroxycholestanoic acid ; ERG ; electroretinogram ; G-tube ; gastrostomy tube ; IRD ; infantile Refsum disease ; LC-MS/MS ; liquid chromatography/tandem mass spectrometry ; NALD ; neonatal adrenoleukodystrophy ; OCT ; optical coherence tomography ; PBD ; peroxisome biogenesis disorder ; PBD-ZSD ; peroxisome biogenesis disorder-Zellweger spectrum disorder ; THCA ; trihydroxycholestanoic acid ; VLCFA ; very long chain fatty

刊名：Molecular Genetics and Metabolism

出版年：2016

8.Targeted metabolomic profiling indicates structure-based perturbations in serum phospholipids in children with acetaminophen overdose

作者：Sudeepa Bhattacharyya^a ; ^b ; ^{SBhattacharyya2@uams.edu} ; Lisa Pence^c ; ^{Lisa.Pence@fda.hhs.gov} ; Ke Yan^d ; ^kyan@mcw.edu ; Pritmohinder Gill^a ; ^{PSGill@uams.edu} ; Chunqiao Luo^a ; ^{CLuo@uams.edu} ; Lynda G. Letzig^a ; ^{LetzigLyndaG@uams.edu} ; Pippa M. Simpson^d ; ^{psimpson@mcw.edu} ; Gregory L. Kearns^a ; ^{KearnsGL@archildrens.org} ; Richard D. Beger^c ; ^{Richard.beger@fda.hhs.gov} ; Laura P. James^a ; ^{JamesLauraP@uams.edu}

关键词：Metabolomics ; Phospholipids ; Acetaminophen ; Hepatotoxicity ; Drug

刊名：Toxicology Reports

出版年：2016

9.CYP4F2 affects phenotypic outcome in adrenoleukodystrophy by modulating the clearance of very long-chain fatty acids

作者：Catherine E. van Engen^a ; Rob Ofman^a ; Inge M.E. Dijkstra^a ; Tessa Jacobs van Goethem^a ; Eveline Verheij^a ; Jennifer Varin^b ; Michel Vidaud^b ; Ronald J.A. Wanders^a ; Patrick Aubourg^c ; ^d ; ¹ ; Stephan Kemp^a ; ¹ ; ^{s.kemp@amc.uva.nl" class="auth_mail" title="E-mail the corresponding author} ; Mathieu Barbier^c ; ¹ ; ²

关键词：Adrenoleukodystrophy ; Modifier gene ; Dicarboxylic acids ; Cytochrome P450 ; Omega-oxidation ; Peroxisomes

刊名：Biochimica et Biophysica Acta (BBA) - Molecular Basis of Disease

出版年：2016

10.Plant sphingolipids: Their importance in cellular organization and adaption

作者：Louise V. Michaelson^a ; ^{louise.michaelson@rothamsted.ac.uk" class="auth_mail" title="E-mail the corresponding author} ; ; Johnathan A. Napier^a ; ^{Johnathan.Napier@rothamsted.ac.uk" class="auth_mail" title="E-mail the corresponding author} ; ; Diana Molino^b ; ^{dmolino@gmail.com" class="auth_mail" title="E-mail the corresponding author} ; Jean-Denis Faure^c ; ^d ; ^{Jean-Denis.Faure@versailles.inra.fr" class="auth_mail" title="E-mail the corresponding author} ;

关键词：Fatty acid ; Long chain base ; Glycans ; Membrane ; Phosphorylation

刊名：Biochimica et Biophysica Acta (BBA)-Molecular and Cell Biology of Lipids

出版年：2016

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